ORTHOLOGY: K01942
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Entry
K01942 KO
Symbol
HLCS
Name
biotin---protein ligase [EC:
6.3.4.9
6.3.4.10
6.3.4.11
6.3.4.15
]
Pathway
map00780
Biotin metabolism
map01100
Metabolic pathways
Reaction
R01074
biotin:CoA ligase (AMP-forming)
R05145
biotinyl-5'-AMP:apo-[carboxylase] ligase (AMP-forming)
Disease
H00180
Holocarboxylase synthetase deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09108 Metabolism of cofactors and vitamins
00780 Biotin metabolism
K01942 HLCS; biotin---protein ligase
Enzymes [BR:
ko01000
]
6. Ligases
6.3 Forming carbon-nitrogen bonds
6.3.4 Other carbon-nitrogen ligases
6.3.4.9 biotin---[methylmalonyl-CoA-carboxytransferase] ligase
K01942 HLCS; biotin---protein ligase
6.3.4.10 biotin---[propionyl-CoA-carboxylase (ATP-hydrolysing)] ligase
K01942 HLCS; biotin---protein ligase
6.3.4.11 biotin---[methylcrotonoyl-CoA-carboxylase] ligase
K01942 HLCS; biotin---protein ligase
6.3.4.15 biotin---[biotin carboxyl-carrier protein] ligase
K01942 HLCS; biotin---protein ligase
BRITE hierarchy
Other DBs
GO:
0004079
0004080
0004078
0004077
Genes
HSA:
3141
(HLCS)
PTR:
473989
(HLCS)
PPS:
100985942
(HLCS)
GGO:
101135438
(HLCS)
PON:
100457062
(HLCS)
PPYG:
129022436
(HLCS)
NLE:
100599352
(HLCS)
HMH:
116482569
(HLCS)
SSYN:
129482980
(HLCS)
MCC:
694733
(HLCS)
MCF:
102133502
(HLCS)
MTHB:
126951553
MNI:
105472658
(HLCS)
CSAB:
103218635
(HLCS)
CATY:
105575421
(HLCS)
PANU:
101013764
(HLCS)
TGE:
112621212
(HLCS)
MLEU:
105544999
(HLCS)
RRO:
104679174
(HLCS)
RBB:
108543829
(HLCS)
TFN:
117095757
(HLCS)
PTEH:
111525767
(HLCS)
CANG:
105520341
(HLCS)
CJC:
100388312
(HLCS)
SBQ:
101045875
(HLCS)
CIMI:
108302561
(HLCS)
ANAN:
105712556
(HLCS)
CSYR:
103254137
(HLCS)
MMUR:
105881298
(HLCS)
LCAT:
123630731
(HLCS)
PCOQ:
105806888
(HLCS)
OGA:
100962733
(HLCS)
MMU:
110948
(Hlcs)
MCAL:
110311917
(Hlcs)
MPAH:
110329965
(Hlcs)
RNO:
288240
(Hlcs)
MCOC:
116086167
(Hlcs)
ANU:
117718128
(Hlcs)
ASYL:
127665619
(Hlcs)
MUN:
110560965
(Hlcs)
CGE:
100752840
(Hlcs)
MAUA:
101825408
(Hlcs)
PROB:
127227544
(Hlcs)
PLEU:
114700373
(Hlcs)
MORG:
121461742
(Hlcs)
MFOT:
126513580
AAMP:
119825079
(Hlcs)
NGI:
103750093
103750102
HGL:
101722847
(Hlcs)
CPOC:
100716230
(Hlcs)
CCAN:
109693415
(Hlcs)
DORD:
105994008
(Hlcs)
DSP:
122114310
(Hlcs)
PLOP:
125351465
(Hlcs)
NCAR:
124992503
MMMA:
107136469
(Hlcs)
ITI:
101956444
(Hlcs)
OCU:
100349035
OPI:
101523312
(HLCS)
TUP:
102498435
(HLCS)
CFA:
478412
(HLCS)
CLUD:
112661919
(HLCS)
VVP:
112911371
(HLCS)
VLG:
121479299
(HLCS)
NPO:
129502090
(HLCS)
AML:
100464483
(HLCS)
UMR:
103673150
(HLCS)
UAH:
113260107
(HLCS)
UAR:
123802684
(HLCS)
ELK:
111155824
LLV:
125094597
MPUF:
101682919
(HLCS)
MNP:
132012389
(HLCS)
MLK:
131825361
(HLCS)
NVS:
122908298
(HLCS)
ORO:
101363115
101368585
(HLCS)
EJU:
114218940
(HLCS)
ZCA:
113917206
(HLCS)
MLX:
118018863
(HLCS)
NSU:
110570073
(HLCS)
LWW:
102735699
(HLCS)
FCA:
101100992
(HLCS)
PYU:
121035949
(HLCS)
PCOO:
112850350
(HLCS)
PBG:
122491180
(HLCS)
PVIV:
125174960
(HLCS)
LRUF:
124526095
LGF:
123610592
(HLCS)
AJU:
106966985
PTG:
102964368
(HLCS)
PPAD:
109249774
(HLCS)
PUC:
125920748
PLEZ:
122229396
(HLCS)
HHV:
120229710
(HLCS)
BTA:
534247
(HLCS)
BOM:
102276987
(HLCS)
BIU:
109561544
(HLCS)
109563420
BBUB:
102407054
(HLCS)
BBIS:
104984888
(HLCS)
CHX:
102179708
(HLCS)
OAS:
101109588
(HLCS)
BTAX:
128056219
(HLCS)
CSUM:
138079548
(HLCS)
ODA:
120880672
(HLCS)
MREE:
136173765
(HLCS)
OVR:
110123114
(HLCS)
MBEZ:
129549140
(HLCS)
SSC:
100515056
(HLCS)
CFR:
102520771
(HLCS)
CBAI:
105070401
(HLCS)
CDK:
105089839
(HLCS)
VPC:
102538594
(HLCS)
BACU:
103015318
(HLCS)
BMUS:
118894378
(HLCS)
LVE:
103086335
(HLCS)
OOR:
101281208
(HLCS)
LALB:
132521334
(HLCS)
DLE:
111163877
(HLCS)
PCAD:
102981930
(HLCS)
114485348
PSIU:
116753145
(HLCS)
NASI:
112408673
(HLCS)
ECB:
100061132
(HLCS)
EPZ:
103550461
(HLCS)
EAI:
106831403
(HLCS)
MYB:
102263271
(HLCS)
MYD:
102765347
(HLCS)
MMYO:
118675452
(HLCS)
MLF:
102440948
(HLCS)
MDT:
132229868
(HLCS)
MYUM:
139004300
(HLCS)
PKL:
118723485
(HLCS)
EFUS:
103289910
(HLCS)
MNA:
107543170
(HLCS)
DRO:
112305753
(HLCS)
SHON:
118983280
(HLCS)
AJM:
119035750
(HLCS)
PDIC:
114490841
(HLCS)
PHAS:
123828033
(HLCS)
MMF:
118617233
(HLCS)
PPAM:
129074398
(HLCS)
HAI:
109391229
(HLCS)
RFQ:
117034459
(HLCS)
PALE:
102889335
(HLCS)
PGIG:
120598588
(HLCS)
PVP:
105295819
(HLCS)
RAY:
107499284
(HLCS)
MJV:
108398522
(HLCS)
TOD:
119257083
(HLCS)
SARA:
101557365
(HLCS)
SFUM:
130028704
(HLCS)
SETR:
126025590
(HLCS)
LAV:
100666961
(HLCS)
TMU:
101340265
ETF:
101656844
(HLCS)
DNM:
101417266
(HLCS)
MDO:
100012694
(HLCS)
GAS:
123242479
(HLCS)
SHR:
100914711
(HLCS)
AFZ:
127553814
PCW:
110214863
(HLCS)
TVP:
118837860
(HLCS)
PBRV:
138142045
(HLCS)
OAA:
120637974
(HLCS)
TACU:
119945254
(HLCS)
GGA:
418516
(HLCS)
PCOC:
116242079
(HLCS)
MGP:
100544537
(HLCS)
CJO:
107323321
(HLCS)
TPAI:
128076321
(HLCS)
LMUT:
125684740
(HLCS)
NMEL:
110402806
(HLCS)
APLA:
101793696
(HLCS)
ACYG:
106036092
(HLCS)
CATA:
118247748
(HLCS)
AFUL:
116493828
(HLCS)
TGU:
105758711
(HLCS)
LSR:
110469057
(HLCS)
SCAN:
108961921
(HLCS)
PMOA:
120511785
(HLCS)
OTC:
121333572
(HLCS)
PRUF:
121364465
(HLCS)
ATRC:
139591498
(HLCS)
GFR:
102039791
(HLCS)
FAB:
101811028
(HLCS)
OMA:
130262854
(HLCS)
PHI:
102113505
(HLCS)
PMAJ:
107202517
(HLCS)
CCAE:
111928640
(HLCS)
CCW:
104696775
(HLCS)
CBRC:
103617033
(HLCS)
ACOE:
138108054
(HLCS)
ETL:
114070498
(HLCS)
114071342
114072950
ZLE:
135444066
(HLCS)
ACHL:
103801071
(HLCS)
SVG:
106855735
(HLCS)
MMEA:
130580001
(HLCS)
HRT:
120747874
SATI:
136358224
(HLCS)
CCIC:
134058134
(HLCS)
FPG:
101921711
(HLCS)
FCH:
102053171
(HLCS)
CCRI:
104161458
NNT:
104401697
SHAB:
115603744
(HLCS)
ACUN:
113482863
(HLCS)
TALA:
104367106
(HLCS)
ACHC:
115343774
(HLCS)
HALD:
104312696
HLE:
104839811
(HLCS)
AGEN:
126053138
HHAR:
128144882
(HLCS)
GCL:
127024079
CSTI:
104553000
LDI:
104354894
MNB:
103771810
(HLCS)
DPUB:
104304944
(HLCS)
PPUS:
135180180
(HLCS)
AVIT:
104273981
BRHI:
104491950
EGZ:
104128244
(HLCS)
NNI:
104020182
(HLCS)
PCRI:
104037019
PCAO:
104049438
(HLCS)
PADL:
103920277
(HLCS)
AFOR:
103901992
(HLCS)
FGA:
104072328
GSTE:
104253174
CLV:
102093696
(HLCS)
MUI:
104543252
(HLCS)
PGUU:
104460842
PLET:
104623306
(HLCS)
EHS:
104513294
CMAC:
104484074
CUCA:
104064784
(HLCS)
TEO:
104375606
(HLCS)
BREG:
104634557
OHA:
104327716
(HLCS)
ACAR:
104519611
(HLCS)
CPEA:
104391198
(HLCS)
CVF:
104292009
(HLCS)
RTD:
128910822
(HLCS)
CRID:
134520401
(HLCS)
AAM:
106494968
(HLCS)
AROW:
112971860
(HLCS)
NPD:
112959086
(HLCS)
TGT:
104572491
104573238
DNE:
112996144
(HLCS)
SCAM:
104139431
(HLCS)
ASN:
102384054
(HLCS)
AMJ:
102565173
(HLCS)
CPOO:
109305810
(HLCS)
GGN:
109302688
(HLCS)
PSS:
102452909
(HLCS)
CMY:
102944554
(HLCS)
CCAY:
125643891
(HLCS)
DCC:
119859772
(HLCS)
CPIC:
101934162
(HLCS)
TST:
117888291
CABI:
116834913
(HLCS)
MRV:
120405524
(HLCS)
ACS:
100562676
(hlcs)
ASAO:
132771858
(HLCS)
PVT:
110076819
(HLCS)
SUND:
121924901
(HLCS)
PBI:
103067600
(HLCS)
PMUR:
107296825
(HLCS)
CTIG:
120320378
(HLCS)
TSR:
106540930
(HLCS)
PGUT:
117679791
(HLCS)
APRI:
131199126
(HLCS)
PTEX:
113436240
(HLCS)
NSS:
113409904
(HLCS)
VKO:
123028983
(HLCS)
PMUA:
114596081
(HLCS)
PRAF:
128413015
(HLCS)
ZVI:
118085627
(HLCS)
HCG:
128350247
(HLCS)
GJA:
107116049
(HLCS)
STOW:
125432224
(HLCS)
EMC:
129325853
(HLCS)
XLA:
108707861
(hlcs.L)
XTR:
100492512
(hlcs)
NPR:
108785966
(HLCS)
RTEM:
120927941
(HLCS)
BBUF:
120994491
(HLCS)
BGAR:
122930793
122932980
PWL:
138248704
(HLCS)
MUO:
115469498
(HLCS)
GSH:
117362813
(HLCS)
DRE:
337784
(hlcs)
SRX:
107747605
(hlcs)
SANH:
107676487
(hlcs)
SGH:
107572952
(hlcs)
CCAR:
109097448
(hlcs)
CAUA:
113054772
CGIB:
128013317
128020687
128020931
PTET:
122333922
(hlcs)
LROH:
127171952
(hlcs)
OMC:
131548399
(hlcs)
PPRM:
120478423
(hlcs)
MAMB:
125262586
(hlcs)
CIDE:
127521941
CERY:
137028454
(hlcs)
MASI:
127432710
TROS:
130545865
(hlcs)
TDW:
130411613
(hlcs)
MANU:
129446353
(hlcs)
PDAB:
135746321
(hlcs)
IPU:
108277209
IFU:
128620758
(hlcs)
PHYP:
113543599
(hlcs)
SMEO:
124393475
(hlcs)
TFD:
113645674
(hlcs)
TVC:
132863142
(hlcs)
CGAR:
128505711
(hlcs)
NGRA:
132873503
(hlcs)
TRN:
134332292
(hlcs)
AMEX:
103022047
(hlcs)
CMAO:
118824639
(hlcs)
EEE:
113581671
(hlcs)
CHAR:
105902089
(hlcs)
SPIL:
134080175
(hlcs)
TRU:
101061285
(hlcs)
TFS:
130537374
(hlcs)
TNG:
GSTEN00016316G001
LCO:
104937128
(hlcs)
NCC:
104958355
(hlcs)
TBEN:
117469538
(hlcs)
CGOB:
115019227
(hlcs)
PGEO:
117458563
(hlcs)
GACU:
117553008
(hlcs)
EMAC:
134872728
(hlcs)
ELY:
117266071
(hlcs)
EFO:
125897955
(hlcs)
PLEP:
121952414
(hlcs)
SLUC:
116058207
(hlcs)
ECRA:
117955796
(hlcs)
ESP:
116700468
(hlcs)
PFLV:
114567320
(hlcs)
GAT:
120822345
(hlcs)
PPUG:
119215381
(hlcs)
AFB:
129113453
(hlcs)
CLUM:
117742450
(hlcs)
PSWI:
130211670
(hlcs)
CANA:
137802991
(hlcs)
CVE:
137880137
(hlcs)
MSAM:
119895079
(hlcs)
SCHU:
122888245
(hlcs)
SPUL:
138594647
(hlcs)
LMIX:
132988371
(hlcs)
ALAT:
119031285
(hlcs)
ASTR:
137605884
(hlcs)
MZE:
101470218
(hlcs)
ONL:
100710097
(hlcs)
OAU:
116335319
(hlcs)
OLA:
101169801
(hlcs)
OML:
112142766
(hlcs)
CSAI:
133459538
(hlcs)
XMA:
102227719
(hlcs)
XCO:
114153743
(hlcs)
XHE:
116727964
(hlcs)
PRET:
103476369
(hlcs)
PFOR:
103130816
PLAI:
106941182
PMEI:
106906378
GAF:
122845331
(hlcs)
PPRL:
129354000
(hlcs)
CVG:
107100031
(hlcs)
CTUL:
119791207
(hlcs)
GMU:
124876218
(hlcs)
NFU:
107386340
(hlcs)
KMR:
108247189
ALIM:
106534551
(hlcs)
NWH:
119420346
(hlcs)
EJA:
138207637
(hlcs)
BFRE:
138614877
(hlcs)
MCEP:
125021309
(hlcS)
CSEM:
103395776
(hlcs)
POV:
109642009
(hlcs)
SSEN:
122779783
(hlcs)
SSOE:
131458724
(hlcs)
HHIP:
117774943
(hlcs)
HSP:
118122116
(hlcs)
PPLT:
128456994
(hlcs)
SMAU:
118300730
(hlcs)
LCF:
108900070
SDU:
111234598
(hlcs)
SLAL:
111653972
(hlcs)
XGL:
120802396
(hlcs)
HCQ:
109519595
(hlcs)
SSCV:
125986647
(hlcs)
SBIA:
133491389
(hlcs)
PEE:
133415707
(hlcs)
PTAO:
133467365
(hlcs)
BPEC:
110170317
(hlcs)
MALB:
109972019
(hlcs)
BSPL:
114869291
(hlcs)
SJO:
128371873
(hlcs)
SSCO:
133994128
(hlcs)
GMH:
115546761
(hlcs)
SASA:
106567688
(hlcs)
STRU:
115148757
(hlcs)
OTW:
112257954
(hlcs)
OMY:
110537572
(hlcs)
OGO:
123999580
(hlcs)
ONE:
115105454
(hlcs)
OKI:
109892826
OKE:
118390677
118391077
(hlcs)
OMM:
135548695
OCLA:
139423181
SALP:
111980678
(hlcs)
SNH:
120030996
(hlcs)
CCLU:
121551977
ELS:
105023991
(hlcs)
SFM:
108936248
(hlcs)
PKI:
111855789
111858423
(hlcs)
AANG:
118235918
(hlcs)
AROT:
135263322
(hlcs)
CCOG:
133134123
(hlcs)
LOC:
102690116
(hlcs)
PSPA:
121302870
(hlcs)
ARUT:
117406319
117407164
PSEX:
120523272
(hlcs)
LCM:
102347440
(HLCS)
CMK:
103188738
(hlcs)
RTP:
109936700
(hlcs)
CPLA:
122555338
(hlcs)
HOC:
132821165
(hlcs)
LERI:
129703015
(hlcs)
PMRN:
116952927
(HLCS)
LRJ:
133354263
(HLCS)
BFO:
118422809
118423079
BBEL:
109464518
CIN:
100179742
SCLV:
120336784
SPU:
577740
LPIC:
129259703
AJJ:
139962523
APLC:
110986169
ARUN:
117296532
AAMU:
139947097
AFIL:
140157417
SKO:
100369411
PFLL:
139142158
DME:
Dmel_CG14670
(Hcs)
DER:
6552203
DSI:
Dsimw501_GD19789
(Dsim_GD19789)
DYA:
Dyak_GE25471
DSR:
110177272
DPO:
6897601
DPE:
6591344
DMN:
108155261
DWI:
6647187
DGR:
6563879
DMO:
Dmoj_GI23080
DAZ:
108614926
DNV:
108656012
DHE:
111603564
CCAT:
101453066
BOD:
106618089
BDR:
105225980
RZE:
108360017
AOQ:
129241539
ALUD:
128865050
TDA:
119680235
SCAC:
106086242
LCQ:
111680170
LSQ:
119606134
CVJ:
135949540
(Hcs)
GFS:
119642639
ECOE:
129943491
CLON:
129608152
HIS:
119660409
AGA:
1281690
ACOZ:
120949731
AARA:
120896139
AMER:
121603568
ASTE:
118505163
AMAP:
126556905
AFUN:
125762356
AMOU:
128309757
ACOS:
131259110
AAG:
5571860
AALB:
109404810
ASUA:
134217547
CQU:
CpipJ_CPIJ007071
CpipJ_CPIJ007072
CPII:
120422427
CNS:
116339785
BCOO:
119074323
LLL:
129788565
PPAP:
129800692
AME:
411759
ACER:
107996086
ALAB:
122719799
ADR:
102675016
AFLR:
100872695
BIM:
100741269
BBIF:
117216160
BVK:
117231240
BVAN:
117155110
BHUN:
126872904
BTER:
100642502
BAFF:
126923588
BPYO:
122574687
BPAS:
132913253
FVI:
122527804
CCAL:
113464824
OBB:
114881255
MGEN:
117224851
NMEA:
116427632
CGIG:
122396269
SOC:
105208017
MPHA:
105832368
AEC:
105150986
ACEP:
105619994
105625408
PBAR:
105427000
VEM:
105570280
COBS:
139104873
(Hcs)
TLN:
139810950
(Hcs)
HST:
105187433
DQU:
106752243
CFO:
105254823
FEX:
115245250
PMEC:
138933490
(Hcs)
LHU:
105676227
(Hcs)
PGC:
109853482
OBO:
105284641
PCF:
106785970
PFUC:
122519663
VPS:
122630628
VCRB:
124424283
VVE:
124950477
NVI:
100120765
CSOL:
105362029
TPRE:
106659272
LHT:
122509053
LBD:
127289881
MDL:
103574421
CGLO:
123269121
FAS:
105273724
DAM:
107038805
AGIF:
122856527
VCAN:
122413677
CCIN:
107265728
DSM:
124409941
NPT:
124216402
(Hcs)
NFB:
124181541
NLO:
107220495
NVG:
124303826
AROA:
105690535
TCA:
100141937
TMOL:
138129253
(Hcs)
DPA:
109541261
ESIM:
136417998
(Hcs)
EFOR:
136342532
(Hcs)
SOY:
115877088
AGRG:
126748915
CSET:
123319879
HAXR:
123675586
AGB:
108907126
LDC:
111507580
DVV:
126880020
NVL:
108566076
APLN:
108744963
PPYR:
116161516
OTU:
111419464
BMOR:
101743517
BMAN:
114239389
114249541
MSEX:
115448234
DPL:
KGM_204685
BANY:
112047377
MJU:
123876691
NIQ:
126776565
VCD:
124538847
MCIX:
123663996
PMAC:
106715388
PPOT:
106110370
PXU:
106116842
BPHI:
137920286
(Hcs)
PRAP:
110993032
PBX:
123709651
PNAP:
125054105
ZCE:
119829075
CCRC:
123700865
LSIN:
126970506
AAGE:
121735948
HAW:
110377217
HZE:
124640782
TNL:
113499624
SLIU:
111348888
OFU:
114359388
ONU:
135081876
ATRA:
106131591
GMW:
113520244
PGW:
126379869
LGLY:
125228010
CSTB:
134755946
CFEL:
113383669
CCRN:
123298076
API:
100166501
DNX:
107172306
AGS:
114132498
RMD:
113551631
ACOO:
126843220
DVT:
126900875
BTAB:
109033441
CLEC:
106662760
HHAL:
106678476
NLU:
111048036
111050202
111058010
HVI:
124360713
MQU:
128993152
PHU:
Phum_PHUM492490
FOC:
113208798
TPAL:
117650062
ZNE:
110833334
CSEC:
111863940
BROR:
134537355
IEL:
124168760
HAMR:
139688193
(Hcs)
FCD:
110853379
DPX:
DAPPUDRAFT_309177
DMK:
116918782
PVM:
113823086
HAME:
121871525
EAF:
111714793
LSM:
121120070
(Hcs)
DSV:
119466650
RSAN:
119376304
RMP:
119176469
VDE:
111247532
VJA:
111262869
TUT:
107366528
DPTE:
113790808
DFR:
124496674
CSCU:
111640237
CVS:
136971810
(Hcs)
PTEP:
107438304
ABRU:
129956860
SDM:
118194372
LPOL:
106461093
106469546
NAI:
NECAME_13444
LOA:
LOAG_17932
HRO:
HELRODRAFT_65278
LGI:
LOTGIDRAFT_171251
PVUL:
126820301
PCAN:
112565926
LSAX:
138961785
BGT:
106068018
GAE:
121372513
HRF:
124117548
HRJ:
124260194
HASI:
137259780
HCRA:
139461253
CRG:
105332906
CANU:
128180210
CVN:
111135439
OED:
125658692
MYI:
110445704
PMAX:
117339376
AIRR:
138334899
MMER:
123552941
RPHI:
132740984
DPOL:
127852785
MAEA:
128238575
OBI:
106879777
106880135
OSN:
115232536
115232587
LJP:
135471718
LAK:
106176354
SMM:
Smp_153150
SHX:
MS3_00002752
OVI:
T265_13178
EGL:
EGR_07298
LLON:
135488253
NVE:
5512817
EPA:
110242401
ATEN:
116291329
ADF:
107339212
MCAZ:
138054530
MFOO:
137996564
PDAM:
113671831
SPIS:
111340632
DGT:
114537726
XEN:
124441389
124441538
124441541
124441869
124442559
124442932
HMG:
105849906
HSY:
130644438
RES:
135685686
AQU:
100632425
ATH:
AT1G37150
(HCS2)
AT2G25710
(HCS1)
ALY:
9314944
9329987
CRB:
17888619
17889810
CSAT:
104703109
104714038
104752205
104752216
EUS:
EUTSA_v10004827mg
EUTSA_v10027838mg
BRP:
103852453
BNA:
106368386
106392404
106409576
125585745
BOE:
106316290
106324724
RSZ:
108805431
108830160
130501420
THJ:
104817066
CPAP:
110816651
CIT:
102613353
CIC:
CICLE_v10001583mg
PVY:
116132147
MINC:
123203292
123206093
123229157
TCC:
18592271
GRA:
105770129
GHI:
107922700
107942037
GAB:
108450088
HSYR:
120154372
120176365
120180396
DZI:
111312328
111315616
EGR:
104450472
120286096
RARG:
115737215
GMX:
100813650
100818402
GSJ:
114410456
114415379
PVU:
137821516
VRA:
106761009
VAR:
108330832
VUN:
114162520
VUM:
124845440
CCAJ:
109794594
APRC:
113873178
MTR:
11411288
TPRA:
123896894
CAM:
101507301
PSAT:
127084121
VVO:
131627382
131641727
LJA:
130735961
ADU:
107460788
AIP:
107606089
AHF:
112706108
112764050
LANG:
109340049
PCIN:
129294455
QSA:
O6P43_015225
FVE:
101294231
AANS:
126784571
RCN:
112170520
PPER:
18789279
PMUM:
103332920
PAVI:
110753343
PDUL:
117626156
MDM:
103401855
103421290
MSYL:
126603611
126632037
PXB:
103933707
103956690
103956969
PCOX:
137718475
137742224
ZJU:
107407500
MNT:
21403054
CSAV:
115723218
CSV:
101206408
CMO:
103489963
BHJ:
120085048
MCHA:
111011837
CMAX:
111487622
CMOS:
111458666
CPEP:
111780897
111808204
RCU:
8260803
8274130
MEAN:
126656452
JCU:
105638886
HBR:
110665565
MESC:
110609471
POP:
7460934
7495112
PEU:
105116743
105127853
PALZ:
118041751
PNZ:
133690846
133693685
JRE:
109013665
CILL:
122310739
CAVE:
132184356
AGLU:
133854275
QSU:
112037475
QLO:
115960411
TWL:
120008484
VVI:
100248922
VRI:
117907121
SLY:
101252547
SPEN:
107003210
SOT:
102584525
SSTN:
125844903
SDUL:
129903254
129903298
CANN:
107850582
107866583
LBB:
132627044
NTA:
107787843
107819232
NSY:
104238135
NTO:
104085554
NAU:
109240668
INI:
109160079
109177408
109183075
109183459
ITR:
116027229
116027249
SIND:
105176554
OEU:
111377897
111383765
EGT:
105974439
SSPL:
121786473
121811335
SMIL:
131011958
SHIS:
125197468
125221333
APAN:
127246467
127249831
HAN:
110865661
ECAD:
122590750
LSV:
111893663
111915583
CCAV:
112507572
DCR:
108196570
108196611
CSIN:
114266663
114315283
RVL:
131307514
AEW:
130776395
DLT:
127799179
127808369
BVG:
104885223
SOE:
110795054
CQI:
110725327
110730819
ATRI:
130809897
MOF:
131162440
MING:
122080726
TSS:
122662409
PSOM:
113346420
113356494
OSA:
4328417
OBR:
102717040
OGL:
127761251
BDI:
100835520
100844888
ATS:
109776075
TDC:
119315816
119324192
TAES:
123132409
123136485
123143975
TUA:
125516143
LPER:
127307896
LRD:
124691197
124691754
SBI:
8074691
ZMA:
103626660
MFLO:
136462754
136471168
SITA:
101752965
101769375
SVS:
117836506
117864159
PVIR:
120661515
PHAI:
112875356
PAUA:
133922620
PDA:
103719623
EGU:
105049052
MUS:
135586607
ZOF:
122047656
DCT:
110102880
PEQ:
110038416
AOF:
109831799
MSIN:
131242542
ACAK:
137938761
NCOL:
116261881
ATR:
18423244
CJF:
131029578
SMO:
SELMODRAFT_80973
SELMODRAFT_88773
PPP:
112286816
CRE:
CHLRE_09g406000v5
CHLRE_12g508852v5
VCN:
VOLCADRAFT_120018
MNG:
MNEG_3981
CSL:
COCSUDRAFT_18259
CVR:
CHLNCDRAFT_135977
CHLNCDRAFT_26827
APRO:
F751_5965
OLU:
OSTLU_119606
(hcs)
OTA:
OT_ostta02g02000
MIS:
MICPUN_72068
MPP:
MICPUCDRAFT_6647
CME:
CYME_CMC080C
SCE:
YDL141W
(BPL1)
SEUB:
DI49_0933
SPAO:
SPAR_D00970
AGO:
AGOS_ADR085W
ERC:
Ecym_8066
KLA:
KLLA0_F05049g
KMX:
KLMA_60514
(BPL1)
LTH:
KLTH0H02024g
VPO:
Kpol_1019p23
ZRO:
ZYRO0F05940g
CGR:
2889255
(GVI51_I03531)
NCS:
NCAS_0A13910
(NCAS0A13910)
NDI:
NDAI_0A02120
(NDAI0A02120)
TPF:
TPHA_0A03060
(TPHA0A03060)
TBL:
TBLA_0F02180
(TBLA0F02180)
TGB:
HG536_0B04920
TDL:
TDEL_0C02310
(TDEL0C02310)
KAF:
KAFR_0B01050
(KAFR0B01050)
KNG:
KNAG_0C03960
(KNAG0C03960)
ZMK:
HG535_0E04840
SLUD:
SCDLUD_000269
DHA:
DEHA2A13750g
PIC:
PICST_69676
(BPL1)
PGU:
PGUG_01114
SPAA:
SPAPADRAFT_48797
LEL:
PVL30_002335
(BPL1)
LBG:
92207224
(LODBEIA_P20280)
CAL:
CAALFM_CR10620CA
(CaO19.7645)
CTP:
CTRG_05783
COT:
CORT_0A05280
CORT_0D00250
CDU:
CD36_35420
CTEN:
18248928
(BPL1)
CLU:
CLUG_02270
CLUS:
A9F13_02g00264
CAUR:
CJI96_0005147
ASAU:
88172704
(PUMCH_001639)
PPA:
PAS_chr3_0569
PKZ:
C5L36_0B05860
BNN:
FOA43_002895
BBRX:
BRETT_005194
OPA:
HPODL_02585
YLI:
2912036
(YALI2_E01146g)
SLB:
AWJ20_1398
(BPL1)
NCR:
NCU05516
NTE:
NEUTE1DRAFT124604
(NEUTE1DRAFT_124604)
SMP:
10807355
(SMAC4_00725)
PAN:
PODANSg2869
PBEL:
QC761_403290
(BPL1)
PPSD:
QC762_403290
(BPL1)
PPSP:
QC763_403290
(BPL1)
PPSA:
QC764_403290
(BPL1)
TTT:
THITE_2110501
MTM:
MYCTH_2119403
CTHR:
CTHT_0044660
RTHE:
98126609
(VTJ83DRAFT_5372)
MGR:
MGG_00436
PPEI:
PpBr36_08732
PGRI:
PgNI_08915
TMN:
UCRPA7_1182
SSCK:
SPSK_02214
FGR:
FGSG_08329
FPU:
FPSE_09477
FPOA:
FPOAC1_004402
FVN:
FVRRES_04912
FVR:
FVEG_02363
FOX:
FOXG_03496
NHE:
NECHADRAFT_36078
FFC:
NCS54_00370100
FKR:
NCS57_00375400
FMU:
J7337_008705
TRE:
TRIREDRAFT_77714
TRR:
M419DRAFT_24638
TATV:
25784141
(TrAtP1_008469)
TASP:
36607621
(TrAFT101_002933)
MAW:
19249106
(BPL1_1)
MAJ:
MAA_02354
MBRN:
26239941
(BPL1)
PCHM:
VFPPC_01307
CMT:
CCM_05319
AMUS:
LMH87_011121
PLJ:
28884721
(PLICBS_005936)
PTKZ:
JDV02_008649
(BPL1)
VAL:
VDBG_09198
VDA:
VDAG_07355
CFJ:
CFIO01_12603
CLUP:
CLUP02_16719
CHIG:
CH63R_06486
CDET:
87947867
(CDEST_11367)
SAPO:
SAPIO_CDS6266
ELA:
UCREL1_3426
PFY:
PFICI_10037
SSL:
SS1G_04467
BFU:
BCIN_01g05670
(Bcbpl1)
MBE:
MBM_09693
PSCO:
LY89DRAFT_451641
GLZ:
GLAREA_00139
ANI:
ANIA_06055
AFM:
AFUA_2G09550
ACT:
ACLA_081340
NFI:
NFIA_085040
AOR:
AO090011000708
ANG:
An16g06410
AFV:
AFLA_008108
ALUC:
AKAW2_70524A
(BPL1)
ACHE:
ACHE_40684A
(BPL1)
APUU:
APUU_11146S
(BPL1)
PCS:
N7525_004424
PDP:
PDIP_65150
POU:
POX_f07849
TMF:
EYB26_004782
TRG:
TRUGW13939_01850
CIM:
CIMG_07858
CPW:
9693336
(BPL1)
URE:
UREG_02182
ABE:
ARB_05148
TVE:
TRV_07820
PBL:
PAAG_06513
PBN:
PADG_00464
AJE:
HCAG_08683
BGH:
BDBG_06963
PNO:
SNOG_08427
PTE:
PTT_11266
PTRR:
6346849
(PtrM4_146620)
BZE:
COCCADRAFT_84592
BSC:
COCSADRAFT_39903
BOR:
COCMIDRAFT_90241
AALT:
CC77DRAFT_1024071
ADAC:
96080346
(ACET3X_000024)
ARAB:
EKO05_0005124
ZTR:
MYCGRDRAFT_67807
PFJ:
MYCFIDRAFT_46146
FFU:
CLAFUR5_10752
CBET:
CB0940_06452
BCOM:
BAUCODRAFT_37668
NPA:
UCRNP2_2382
TML:
GSTUM_00004427001
SPO:
2540476
(bpl1)
SOM:
SOMG_01070
(bpl1)
CNE:
CNC00800
CNB:
CNBC6470
CNG:
CNAG_01565
CGI:
CGB_C1330W
CDEU:
CNBG_9440
CDEP:
91085118
(L203_100904)
KMG:
30162798
(I203_101347)
KNE:
92179657
(IAR55_002398)
TMS:
TREMEDRAFT_40864
TASA:
A1Q1_02988
CCAC:
CcaHIS019_0100680
(BPL1)
TVS:
TRAVEDRAFT_74836
DSQ:
DICSQDRAFT_136396
PCO:
PHACADRAFT_253991
SHS:
STEHIDRAFT_146851
HIR:
HETIRDRAFT_147935
PSQ:
PUNSTDRAFT_59339
ADL:
AURDEDRAFT_111555
FME:
FOMMEDRAFT_74436
GTR:
GLOTRDRAFT_65526
RSX:
RhiXN_10869
LBC:
LACBIDRAFT_317063
CCI:
CC1G_15548
ABP:
AGABI1DRAFT114677
(AGABI1DRAFT_114677)
ABV:
AGABI2DRAFT226601
(AGABI2DRAFT_226601)
MRR:
Moror_6357
MORE:
E1B28_006469
SCM:
SCHCO_02597546
(SCHCODRAFT_02597546)
CPUT:
CONPUDRAFT_124809
SLA:
SERLADRAFT_355394
WSE:
WALSEDRAFT_59378
WIC:
J056_004070
UMA:
UMAG_03839
PFP:
PFL1_06449
SGRA:
EX895_001269
MGL:
MGL_0053
MRT:
MRET_1269
MSYM:
MSY001_1290
PGR:
PGTG_14205
PTRC:
PtA15_9A431
PSTR:
Pst134EA_021178
MLR:
MELLADRAFT_69028
RIE:
OCT59_018828
DDI:
DDB_G0289035
(hlcs3)
DPP:
DICPUDRAFT_18614
DFA:
DFA_05534
(hlcs3)
PIF:
PITG_12194
PSOJ:
PHYSODRAFT_486526
SPAR:
SPRG_09434
GTT:
GUITHDRAFT_144527
» show all
Taxonomy
UniProt
Reference
PMID:
7842009
Authors
Suzuki Y, Aoki Y, Ishida Y, Chiba Y, Iwamatsu A, Kishino T, Niikawa N, Matsubara Y, Narisawa K
Title
Isolation and characterization of mutations in the human holocarboxylase synthetase cDNA.
Journal
Nat Genet 8:122-8 (1994)
DOI:
10.1038/ng1094-122
Sequence
[hsa:
3141
]
Reference
PMID:
7753853
Authors
Leon-Del-Rio A, Leclerc D, Akerman B, Wakamatsu N, Gravel RA
Title
Isolation of a cDNA encoding human holocarboxylase synthetase by functional complementation of a biotin auxotroph of Escherichia coli.
Journal
Proc Natl Acad Sci U S A 92:4626-30 (1995)
DOI:
10.1073/pnas.92.10.4626
LinkDB
All DBs
DBGET
integrated database retrieval system